Comparison of Fibroblasts from Patients Affected by Pseudoxanthoma elasticum (PXE) or by β-Thalassemia with (β-thal-PXE+) and without PXE-Like Clinical Manifestations (β-thal-PXE-)
Abstract
Data di Pubblicazione:
2008
Citazione:
Comparison of Fibroblasts from Patients Affected by Pseudoxanthoma elasticum (PXE) or by β-Thalassemia with (β-thal-PXE+) and without PXE-Like Clinical Manifestations (β-thal-PXE-) / Boraldi, Federica; Paolinelli Devincenzi, Chiara; M. I., Garcia Fernandez; Annovi, Giulia; Quaglino, Daniela; Tiozzo, Roberta; P., Cianciulli; Ronchetti, Ivonne. - In: THE AMERICAN JOURNAL OF PATHOLOGY. - ISSN 0002-9440. - STAMPA. - 173:(2008), pp. S11-RR10-S11-RR10. ( XXIX SIP Congress Rende 10-13 settembre 2008).
Abstract:
The role of altered redox balance in the pathogenesis of PXE-like clinical manifestations in patients affected by beta-thalassemia is discussed.
Tipologia CRIS:
Abstract in Rivista
Keywords:
elastin; calcification; redox balance; oxidative stress; connective tissue; disease
Elenco autori:
Boraldi, Federica; Paolinelli Devincenzi, Chiara; M. I., Garcia Fernandez; Annovi, Giulia; Quaglino, Daniela; Tiozzo, Roberta; P., Cianciulli; Ronchetti, Ivonne
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